Friday 5 April 2013

SYRINGOMYELIA: Causes, Diagnosis and Treatment


SYRINGOMYELIA:
Syringomyelia is the formation of fluid filled cavity or cyst (syrinx) within the spinal cord that may enlarge with time causing damage to the spinal cord along with pain, stiffness and weakness in shoulder, neck, back and legs.

SIGNS AND SYMPTOMS:
Other symptoms include loss of the ability feeling to extremes hot and cold especially in hand, headache, facial pain and numbness, spinal curvature and bowel and bladder function problem. Signs and symptoms may develop with time with, although sudden onset may occur with coughing and straining followed by weakness, progressive loss in sensation and weakness in arms and legs.

COMPLICATIONS:
Complications include scoliosis, motor movements, chronic pain and Horner syndrome. If condition not treated in time it may result in injury to spinal cord.

CAUSES:
·         Chiari formation (congenital abnormality of the brain, in which part of brain tissue may protrude into the Spinal cord).
·         Spinal cord tumor
·         Spinal cord injuries
·         Inflammation surrounding spinal cord
·         Meningitis
·         Arachnoiditis
·         Tethered spinal cord syndrome
·         Spinal scar tissue

DIAGNOSIS:
Syringomyelia is diagnosed by number of ways.
·         Magnetic resonance imaging of spine and spinal cord ( help in beginning stage diagnosis).
·         Electromyography that measures the muscle weakness
·         Cerebrospinal fluid pressure level and analysis of cerebrospinal fluid by performing lumbar puncture
·         Computed axial  tomography that scan patient head to detect any tumor and hydrocephalus
·         Myelogarm

TREATMENT:
Surgery is the only treatment for syrigomyelia.The main purpose of surgery is to provide more space for the cerebellum at the base of skull and cervical spine to treat Chiari formation. Sometimes additional operations are necessary for successful eradication of syringomyelia.
Congenital syringomyelia may require piece of cervical vertebrae at the site of cavity formation to be removed.
If syringomyelia is due to tumor, that result in obstruction then removal of tumor is necessary.
Drainage of cavity (drainage just stop progression, have no concern with the elimination of symptoms associated with syringomyelia) using drainage tubes, catheter and valve .This system is also called shunt.
Physical therapy management depends upon severity and impact of the disease. Neurological examination clears that at which level the syrinx occur. Physical therapy techniques include following:

  I.            RoM (range of motion) stretching and mobilization of neck and upper limb.
II.            Muscle strength
III.            Neck stability
IV.            Balance
V.            Copying
VI.            Occupational therapy


MEDICATION:
·          To alleviate the pain during syringomyelia single or combination of medicines are used; but is not concerned with the removal of syringomyelia.
·         Analgesics are the best ever option to treat syringomyelia. In one pain management plan, an around-the-clock opiate such as fentanyl patches or Oxycontin are used in conjunction with a fast-acting opiate.
·         For classical back pain weak or strong opioids are used such as Tramdol along with medications that relives neuropathic pain symptoms shooting and stabbing pain (neurontin).
·         Cortisteroids, such as prednisolone, or non-steroidal anti-inflammatory drugs may relieve the symptoms but not the deterioration. Long term use of these drugs is not advised.
·         Anticonvulsants, such as gabapentin have been successful in some more severe cases, but they may be very expensive.  Pregabalin, amitriptyline and oral opioids (pethidine or methadone) are alternatives.  Methylsulfonylmethane (MSM) is recommended by some veterinary neurologists as a dietary supplement.
·         Drugs which reduce the production of cerebrospinal fluid, including proton pump inhibitors such as omeprazole, and the diuretic, furosemide (Lasix), and spironolactone, may be useful,but clinical data on their use and effectiveness is lacking.  Carbonic anhydrase inhibitors, such as acetazolamide also serve to decrease the flow of cerebrospinal fluid, but their adverse side effects of abdominal pain, lethargy, and weakness limit long term use.

LIFE STYLE CHANGES:
Avoid such activities that may worse the symptoms of syringomyelia such as
·         Playing high impact sports such as football.
·         Straining during bowel movement
·         Excessive coughing
·         Sky diving

CHINESE ART OF HEALING
Qigong is a traditional form of Chinese energy excise and healing art for the body and mind. Qigong is ideal for re-establishing balance between body and mind and for helping to heal people who are struggling with chronic degenerative conditions such as paralysis, diabetes, and syringomyelia.

 REFERENCES:

                                                                                                                          


          
                                                                                                                                
By: Amna Hafeez

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